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Friday, October 30, 2015

MTHFR and ADHD: Should You Be Tested?

MTHFR is an enzyme , methylenetetrahydrofolate reductase) which is coded for by a gene of the same name.  It has been associated with a number of conditions in numerous small studies, and widely touted, particularly in the naturopathic community, as an important cause of ADHD and other mental disorders.  Others feel that MTHFR testing is just another scam.

How accurate is testing?  How is an abnormal test defined?
There are many variations of the gene for MTHFR.  The important thing to know is that not all variations cause the MTHFR enzyme to function abnormally. Many are normal variants which do not affect the health of the individual.   When the enzyme functions at less than 20% of normal, an individual becomes severely ill, with high levels of homocysteine in the urine, seizures, developmental delay, and muscular dysfunction, but this is extremely rare, with less than 1% of the world's population affected.

The genetic variant associated with ADHD is the A1298C variant, which doesn't do anything to the ability of MTHFR's ability to process folate, produce methyltetrahydrofolate and or moderate homocysteine levels.  Instead it affects the production of tetrahydrobiopterin, which is needed for production of certain neurotransmitters (dopamine, serotonin, and norepinephrine included), among other things like melatonin.  This variant is not associated with heart disease, recurrent pregnancy loss, Alzheimer's disease, neural tube defects (includes spina bifida) or schizophrenia.

Is there any mutation specific treatment that can help people with MTHFR variants with their ADHD?
The short answer to this is, for most patients, we don't know.  No studies have been done to show whether  supplementing with any kind of vitamin or metabolite of a vitamin helps ADHD symptoms in patients with any MTHFR variant.  While it may seem to be sensible to supplement with methylfolate or BH4, there have been many cases in medicine where the sensible thing ended up to be detrimental when clinical studies were done.

In patients who have phenylketonuria (PKU), an uncommon genetic metabolic disease usually detected on newborn screening, small trials indicate that treatment with BH4 (drug name:  sapropterin) may decrease symptoms of inattentiveness.  However, this could be due to it lowering levels of phenylalanine, which accumulates in people who have PKU, but not in people without PKU.

Could treatment be harmful?
Its hard to believe that increasing one's intake of green, leafy vegetables could be harmful.  If anything, at least it should help digestion.  However, taking megadoses could be another story.

If a patient takes BH4 (sapropterin), there can be serious side effects such as bleeding from the stomach and allergic reactions.  Hyperactivity can also occur.  Headache, runny nose, and diarrhea or vomitting have been observed commonly with significant replacement doses used in treating phenylketonuria, a genetic metabolic disease.  Because of the way it works, sapropterin can cause several important drug interactions.

Methylfolate in larger doses may have some mild side effects as well in some patients, such as agitation, anxiety, irritability, nausea, and headache, although usually it does not.
It would seem unnecessary to treat the MTHFR A1298C variant with methylfolate, however, since this variant does not cause problems with the metabolism of folate.

Is there any harm to genetic testing?
Yes.   While your individual health information is protected, there is always the possibility that it could be hacked, leading to a privacy breech. 

Many of the services offering genetic test interpretation are by doctors who do not ever meet you and therefore cannot do as good a job counseling you as to your test results as a doctor who knows you.  This could lead to you making important medical decisions without the right information.  It is important to note that while some genetic variants have been associated with certain diseases, these are still only associations.  We do not know if these genetic variations cause these problems or if there are other factors involved.

Having genetic information about yourself can lead to unpleasant surprises.  When you get tested for MTHFR variants, you get full genome sequencing, which gives you a lot of other information.  One of the most difficult issues may be finding out things that you don't want to know--like that you are not related to your father, or that you are suceptible to a disease that has no cure.

Finally, having interpreted genetic information could become a problem if it is required to be released to an insurance provider.  While you are protected from certain forms of discrimination by the Genetics Information Nondiscrimination Act (GINA), the GINA does not cover life, long term care, or disability insurance.

Bottom line:
Testing for MTHFR does not help us understand or treat a patient's ADHD at this time because of the lack of proven gene specific treatments, the risk of treatments that "make metabolic sense", and because of the inherent risks of genetic testing itself.

References:
"KUVAN® (sapropterin Dihydrochloride) Tablets for Oral Use and Powder for Oral Solution for PKU." BioMarin : Products : KUVAN®. BioMarin Pharmaceutical, Inc., 2015. Web. 26 Oct. 2015.

"Methylenetetrahydrofolate Reductase." Wikipedia. Wikimedia Foundation, 3 Oct. 2015. Web. 26 Oct. 2015.

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